# OnCo record desmoplastic-small-round-cell-tumour (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/desmoplastic-small-round-cell-tumour/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "desmoplastic-small-round-cell-tumour" ;
  schema:name "Desmoplastic small round cell tumour"@en ;
  schema:alternateName "DSRCT"@en, "Desmoplastic small round cell tumor"@en, "Intra-abdominal desmoplastic small round cell tumour"@en, "EWSR1-WT1 sarcoma"@en ;
  schema:description "Desmoplastic small round cell tumour is a very rare sarcoma of adolescents and young men that grows across the lining of the abdomen as many nodules, driven by an EWSR1-WT1 fusion. Treatment is intensive chemotherapy, surgery to remove every nodule, sometimes heated abdominal chemotherapy, and radiotherapy. Most still relapse within three years, so it is treated at a sarcoma centre running trials."@en ;
  schema:url <https://onco.cc/cancers/desmoplastic-small-round-cell-tumour/> ;
  schema:dateModified "2026-09-24"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Desmoplastic_small-round-cell_tumor> ;
  schema:citation <https://www.cancer.gov/types/soft-tissue-sarcoma/patient/child-soft-tissue-treatment-pdq>, <https://doi.org/10.1155/2014/680126>, <https://doi.org/10.3390/cancers13030498> ;
  onco:tag "subtype-page", "wave4", "rare" ;
  onco:related <https://onco.cc/cancers/sarcoma/>, <https://onco.cc/cancers/ewing-sarcoma/>, <https://onco.cc/cancers/rhabdomyosarcoma/>, <https://onco.cc/cancers/peritoneal-mesothelioma/>, <https://onco.cc/cancers/childhood-cancers/>, <https://onco.cc/cancers/adamantinoma/> ;
  onco:technologies <https://onco.cc/technologies/hipec/> ;
  onco:targets <https://onco.cc/targets/wt1/>, <https://onco.cc/targets/pdgfra/> ;
  onco:drugs <https://onco.cc/drugs/vincristine/>, <https://onco.cc/drugs/doxorubicin/>, <https://onco.cc/drugs/cyclophosphamide/>, <https://onco.cc/drugs/ifosfamide/>, <https://onco.cc/drugs/etoposide/>, <https://onco.cc/drugs/pazopanib/>, <https://onco.cc/drugs/sunitinib/> ;
  onco:standardOfCare <https://onco.cc/cancers/sarcoma/>, <https://onco.cc/drugs/vincristine/>, <https://onco.cc/drugs/doxorubicin/>, <https://onco.cc/drugs/cyclophosphamide/>, <https://onco.cc/drugs/ifosfamide/>, <https://onco.cc/drugs/etoposide/>, <https://onco.cc/technologies/hipec/>, <https://onco.cc/drugs/pazopanib/>, <https://onco.cc/drugs/sunitinib/> .