# OnCo record dedifferentiated-chordoma (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/dedifferentiated-chordoma/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "dedifferentiated-chordoma" ;
  schema:name "Dedifferentiated chordoma"@en ;
  schema:alternateName "Chordoma with sarcomatous transformation"@en, "Dedifferentiated chordoma (high-grade sarcoma in a chordoma)"@en ;
  schema:description "Dedifferentiated chordoma is a rare form of chordoma in which part of the tumour has turned into a high-grade sarcoma, usually after recurrence or radiotherapy but sometimes from the start. The sarcoma part decides the outcome and made up 3 to 95 percent of the tumour in the defining series, smaller areas doing better, so it is treated with surgery and sarcoma chemotherapy."@en ;
  schema:url <https://onco.cc/cancers/dedifferentiated-chordoma/> ;
  schema:dateModified "2026-09-24"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Chordoma> ;
  schema:citation <https://doi.org/10.1097/pas.0000000000001501>, <https://doi.org/10.1302/0301-620x.90b5.20365> ;
  onco:tag "subtype-page", "wave4", "rare" ;
  onco:related <https://onco.cc/cancers/chordoma/>, <https://onco.cc/cancers/poorly-differentiated-chordoma/>, <https://onco.cc/cancers/sarcoma/>, <https://onco.cc/cancers/undifferentiated-pleomorphic-sarcoma/> ;
  onco:technologies <https://onco.cc/technologies/proton-therapy/> ;
  onco:targets <https://onco.cc/targets/tbxt/> ;
  onco:drugs <https://onco.cc/drugs/doxorubicin/> ;
  onco:standardOfCare <https://onco.cc/cancers/chordoma/>, <https://onco.cc/cancers/sarcoma/>, <https://onco.cc/technologies/proton-therapy/>, <https://onco.cc/drugs/doxorubicin/> .