# OnCo record angioimmunoblastic-t-cell-lymphoma (cancer). Data CC BY-NC 4.0, attribute "Data from OnCo (onco.cc)". Whole corpus: https://onco.cc/api/v1/onco.nt
@prefix schema: <https://schema.org/> .
@prefix onco: <https://onco.cc/ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .

<https://onco.cc/cancers/angioimmunoblastic-t-cell-lymphoma/>
  a schema:MedicalCondition ;
  onco:kind "cancer" ;
  schema:identifier "angioimmunoblastic-t-cell-lymphoma" ;
  schema:name "Nodal T-follicular helper cell lymphoma, angioimmunoblastic type (angioimmunoblastic T-cell lymphoma)"@en ;
  schema:alternateName "Angioimmunoblastic T-cell lymphoma"@en, "AITL"@en, "Nodal TFH lymphoma"@en, "Nodal TFH lymphoma (angioimmunoblastic type)"@en, "nTFHL-AI"@en, "Angioimmunoblastic lymphadenopathy with dysproteinaemia"@en ;
  schema:description "Angioimmunoblastic T-cell lymphoma, now called nodal T-follicular helper cell lymphoma of angioimmunoblastic type, is one of the commonest T-cell lymphomas and mostly affects people over 60. It presents with widespread swollen nodes, fever, rash and immune upsets such as anaemia; about four in ten people are alive five years after chemotherapy, more after a transplant in first remission."@en ;
  schema:url <https://onco.cc/cancers/angioimmunoblastic-t-cell-lymphoma/> ;
  schema:dateModified "2026-09-24"^^xsd:date ;
  schema:sameAs <https://en.wikipedia.org/wiki/Angioimmunoblastic_T-cell_lymphoma> ;
  schema:citation <https://www.cancer.gov/types/lymphoma/patient/adult-nhl-treatment-pdq>, <https://doi.org/10.1038/s41375-022-01620-2>, <https://doi.org/10.1200/jco.2011.37.3647>, <https://doi.org/10.1182/blood.2020010387> ;
  onco:tag "subtype-page", "wave4", "haematologic", "rare" ;
  onco:related <https://onco.cc/cancers/peripheral-t-cell-lymphoma/>, <https://onco.cc/cancers/hepatosplenic-t-cell-lymphoma/>, <https://onco.cc/cancers/cutaneous-t-cell-lymphoma/>, <https://onco.cc/cancers/dlbcl/>, <https://onco.cc/biomarkers/rhoa-g17v/>, <https://onco.cc/biomarkers/ig-tcr-clonality/> ;
  onco:technologies <https://onco.cc/technologies/cgp/>, <https://onco.cc/technologies/clonality-testing/>, <https://onco.cc/technologies/histopathology-ihc/> ;
  onco:targets <https://onco.cc/targets/rhoa/>, <https://onco.cc/targets/tet2/>, <https://onco.cc/targets/dnmt3a/>, <https://onco.cc/targets/fyn/>, <https://onco.cc/targets/b2m/>, <https://onco.cc/targets/cd58/>, <https://onco.cc/targets/cd30/>, <https://onco.cc/targets/cd52/> ;
  onco:drugs <https://onco.cc/drugs/cyclophosphamide/>, <https://onco.cc/drugs/romidepsin/>, <https://onco.cc/drugs/belinostat/>, <https://onco.cc/drugs/pralatrexate/>, <https://onco.cc/drugs/azacitidine/>, <https://onco.cc/drugs/brentuximab-vedotin/> ;
  onco:pathways <https://onco.cc/pathways/epigenetic-reprogramming/>, <https://onco.cc/pathways/clonal-haematopoiesis/>, <https://onco.cc/pathways/jak-stat/> ;
  onco:terms <https://onco.cc/terms/r-chop/>, <https://onco.cc/terms/lymphoma-tx-regimen-alphabet/>, <https://onco.cc/terms/lymphoma-tx-transplant-role/>, <https://onco.cc/terms/lymphoma-tx-pjp-and-infection-prophylaxis/>, <https://onco.cc/terms/lymphoma-bio-lineage-antigen-cost/> ;
  onco:trials <https://onco.cc/trials/nct06522737/> ;
  onco:standardOfCare <https://onco.cc/cancers/peripheral-t-cell-lymphoma/>, <https://onco.cc/drugs/cyclophosphamide/>, <https://onco.cc/terms/r-chop/>, <https://onco.cc/drugs/romidepsin/>, <https://onco.cc/drugs/belinostat/>, <https://onco.cc/drugs/pralatrexate/>, <https://onco.cc/drugs/azacitidine/>, <https://onco.cc/drugs/brentuximab-vedotin/>, <https://onco.cc/trials/nct06522737/>, <https://onco.cc/terms/lymphoma-tx-regimen-alphabet/>, <https://onco.cc/drugs/brentuximab-vedotin/>, <https://onco.cc/drugs/cyclophosphamide/>, <https://onco.cc/drugs/doxorubicin/>, <https://onco.cc/drugs/vincristine/>, <https://onco.cc/drugs/prednisone/>, <https://onco.cc/drugs/etoposide/>, <https://onco.cc/drugs/romidepsin/>, <https://onco.cc/drugs/belinostat/>, <https://onco.cc/technologies/autologous-stem-cell-transplant/>, <https://onco.cc/terms/lymphoma-tx-pjp-and-infection-prophylaxis/>, <https://onco.cc/terms/lymphoma-tx-transplant-role/> .
